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顺乌头酸酶

删除1,317字节, 2017年1月22日 (日) 18:55
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{{enzyme| Name = 乌头酸水合酶| EC_number = 4.2.1.3| CAS_number = 9024-25-3| IUBMB_EC_number = 4/2/1/3| GO_code = 0003994| image = 7ACN.jpg| width = | caption = 结合铁-硫簇的猪顺乌头酸酶插画。按二级结构将蛋白质着色,铁原子以蓝色表示,硫原子以红色表示<ref name="pmid1547214">; </ref>。}}{{Infobox protein family| Symbol = 顺乌头酸酶| Name = 顺乌头酸酶家族<br />(乌头酸水合酶)| image = PDB 1aco EBI.jpg| width = | caption = 顺乌头酸酶结构<ref name="pmid8151704">; </ref>。| Pfam = PF00330| InterPro = IPR001030| SMART = | PROSITE = PDOC00423| SCOP = 1aco| TCDB = | OPM family = | OPM protein = }}''''''顺乌头酸酶'''<ref>[http://www.term.gov.cn/pages/homepage/result2.jsp?id=332348&subid=10001798&subject=%E9%85%B6&subsys=%E7%94%9F%E7%89%A9%E5%8C%96%E5%AD%A6%E4%B8%8E%E5%88%86%E5%AD%90%E7%94%9F%E7%89%A9%E5%AD%A6]</ref>'''(,简称为'''[[乌头酸]]酶''',)是一种在三[[羧酸]]循[[环中]][[催化]][[柠檬酸]]通过顺乌头酸中间步骤[[立体专一性]]可逆异构化为[[异柠檬酸]]的酶,这是一个非[[氧化还原]]步骤<ref name=\"pmid8262329\"></ref><ref name=\"pmid11848829\"></ref><ref name=\"pmid11848830\"></ref>。
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从[[细菌]]到人类,顺乌头酸酶都可以被表达出来。人类表达以下两种[[同工酶]]:
{|
| {{protein| Name = 顺乌头酸酶1,可溶性| caption = | image = | width = | HGNCid = 117| Symbol = ACO1| AltSymbols = IREB1| EntrezGene = 48| OMIM = 100880| RefSeq = NM_002197| UniProt = P21399| PDB = | ECnumber = 4.2.1.3| Chromosome = 9| Arm = p| Band = 21.1| LocusSupplementaryData = }}| {{protein| Name = 顺乌头酸酶2,线粒体酶| caption = | image = | width = | HGNCid = 118| Symbol = ACO2| AltSymbols = ACONM| EntrezGene = 50| OMIM = 100850| RefSeq = NM_001098| UniProt = Q99798| PDB = | ECnumber = 4.2.1.3| Chromosome = 22| Arm = q| Band = 13.2| LocusSupplementaryData = }}
|}
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